Idiopathic myelofibrosis with neutrophil myeloperoxidase deficiency: a case report.
نویسندگان
چکیده
We describe a case of idiopathic myelofibrosis with total neutrophil myeloperoxidase deficiency. The combination of this enzymatic defect with myelofibrotic changes in the nuclear shape of neutrophils confers a peculiar appearance on leukograms produced by a Technicon H*1. The clinical course of the disease was shortened by recurrent infections that may be ascribed, at least in part, to reduced leukocyte microbicidal ability.
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ورودعنوان ژورنال:
- Haematologica
دوره 82 4 شماره
صفحات -
تاریخ انتشار 1997